Rare Pulmonary Diseases

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Idiopathic Pulmonary Fibrosis (IPF)

The word “Idiopathic” refers to “of unknown cause” so idiopathic pulmonary fibrosis is one of a Rare Pulmonary Diseases, fibrosis of the lungs without known cause. It is a syndrome of radiologic, pathologic and clinical features of advanced interstitial pulmonary fibrosis and respiratory failure without known cause. It is associated with a histological pattern of usual interstitial pneumonia. It mostly affects middle- aged and older adults and there is no cure. The progress of disease varies from person to person.

Causes
The main Cause of Idiopathic Pulmonary Fibrosis is when people are exposed to something in their environment, for example, certain medicines, or an infection. Sometimes, it runs in family.
Followings are the causes of IPF,
·         Smoke Cigarettes
·         Breathe in wood or metal dust at work or at home
·         Have acid reflux diseases
·         Viral Infections

Symptoms

Followings are the symptoms of IPF that tend to develop gradually and get slowly worse over time,
·         Shortness of Breath
·         A persistent dry cough
·         Tiredness
·         Loss of appetite and weight loss
·         Rounded and Swollen fingertips

Diagnosis

Followings are the diagnosis of IPF,
Chest X-ray
Exercise test
High-resolution CT, or computed tomography
Biopsy        
Pulse oximetry and arterial blood gas tests
Spirometry

Treatment

Treatments for IPF won’t cure the disease, butb it can make ieasier for you to breathe. Followings are some treatments of IPF,
Medicine – Two drugs named “nintedanib” and “pirfenidone” are approved to treat IPF. But these treatment found to be, slow down scarring and damage in your lungs.
Oxygen therapy – In this therapy, you have to breathe oxygen through a mask or prongs that go in your nose. It boosts the oxygen in your blood so you have less shortness of breathe and can be more active.
Pulmonary rehabilitation – For this you have to concern your doctors, nurses and therapists and also focus on exercise, healthy eating, relaxation, stress relief, and ways to save your enegy.



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